Neuro-Otological Findings in Normal Children

Neuro-otological abnormalities in Friedreich's ataxia.

Ten patients with an accepted diagnosis of Friedreich's ataxia have been examined neuro-otologically, and oculomotor, vestibular and auditory function assessed. Brainstem auditory evoked potentials (BAEPs) were also recorded. A high incidence of various eye movement disorders was noted. Some of these were indicative of cerebellar dysfunction. Reduced vestibular function and impaired hearing wer...

Neuro-Otological Aspects of Cerebellar Stroke Syndrome

Cerebellar stroke is a common cause of a vascular vestibular syndrome. Although vertigo ascribed to cerebellar stroke is usually associated with other neurological symptoms or signs, it may mimic acute peripheral vestibulopathy (APV), so called pseudo-APV. The most common pseudo-APV is a cerebellar infarction in the territory of the medial branch of the posterior inferior cerebellar artery (PIC...

Neuro-otological syndromes for the neurologist.

Correspondence to: Dr James Overell, Institute of Neurological Sciences, Southern General Hospital, 1345 Govan Road, Glasgow, G51 4TF; j.overell@clinmed. gla.ac.uk _________________________ N eurologists may be tempted to regard deafness as ‘‘somebody else’s problem’’—generally the cause will lie within the remit of an ear, nose, and throat (ENT) specialist. While such an approach is often reas...

Diagnostic Issues in Tinnitus: a Neuro-otological Perspective

Neuro-Otological and Peripheral Nerve Involvement in Fabry Disease

Fabry disease (FD) is an X-linked lysosomal storage disease, with multisystemic glycosphingolipids deposits. Neuro-otological involvement leading to hearing loss and vestibular dysfunctions has been described, but there is limited information about the frequency, site of lesion, or the relationship with peripheral neuropathy. The aim was to evaluate the presence of auditory and vestibular sympt...